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This significantly updated new edition describes in detail the clinical presentations, diagnosis, and management of a wide range of congenital bleeding disorders. It will assist readers in overcoming the significant challenges involved in clinical and laboratory diagnosis and in providing effective clinical care that makes optimal use of new products, including recombinant factor concentrate. The coverage ranges from hemophilia A and B and von Willebrand disease to rare bleeding disorders such as congenital factor V, factor X, factor XI, and factor XIII deficiency and inherited platelet function disorders. The exceptional attention to rarer conditions is of particular importance given the considerable risk of overlooking them during diagnosis, with potential consequences for disease-related morbidity and mortality. The authors are acknowledged specialists in the field from across the world who have particular expertise in the disorder that they discuss. The book will be of value to hematologists, oncologists, pediatricians, laboratory specialists and technicians, general physicians, and trainees.
Pages i-xvi
Front Matter
Pages 1-1
Pages 3-27
Congenital Bleeding Disorders: Diagnosis and Management
Pages 29-74
Front Matter
Pages 75-75
von Willebrand Disease: An Update on Diagnosis and Treatment
Pages 77-105
Hemophilia A: Diagnosis and Management
Pages 107-143
Hemophilia B: Diagnosis and Management
Pages 145-171
Front Matter
Pages 173-173
Congenital Fibrinogen Disorders, Diagnosis, and Management
Pages 175-190
Congenital Prothrombin Deficiency: Diagnosis and Management
Pages 191-209
Congenital Factor V Deficiency, Diagnosis, and Management
Pages 211-229
Combined Factor V and Factor VIII Deficiency, Diagnosis, and Management
Pages 231-248
Vitamin K-Dependent Coagulation Factors Deficiency, Diagnosis, and Management
Pages 249-258
Congenital Factor VII Deficiency, Diagnosis, and Management
Pages 259-285
Congenital Factor X Deficiency, Diagnosis, and Management
Pages 287-341
Congenital Factor XI Deficiency, Diagnosis and Management
Pages 343-362
Congenital Factor XIII Deficiency, Diagnosis, and Management
Pages 363-375
Front Matter
Pages 377-377
Glanzmann Thrombasthenia: Diagnosis and Management
Pages 379-422
Bernard-Soulier Syndrome: Diagnosis and Management
Pages 423-444
Gray Platelet Syndrome: Diagnosis and Management
Pages 445-463
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